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Issue Date	Title	Author(s)
2007	The Friedreich ataxia GAA repeat expansion mutation induces comparable epigenetic changes in human and transgenic mouse brain and heart tissues	Pook, MA; Al-Mahdawi, S; Mouro Pinto, R; Sandi, C; Trabzuni, D
2006	The GAA triplet-repeat is unstable in the context of the human FXN locus and displays age-dependent expansions in cerebellum and DRG in a transgenic mouse model	Pook, MA; Clark, RM; De Biase, I; Al-Mahdawi, S; Malykhina, AP; Bidichandani, S
2012	Interferon gamma upregulates frataxin and corrects the functional deficits in a Friedreich ataxia model	Tomassini, B; Arcuri, G; Fortuni, S; Sandi, C; Ezzatizadeh, V; Casali, C; Condò, I; Malisan, F; Al-Mahdawi, S; Pook, M; Testi, R
2011	Prolonged treatment with pimelic o-aminobenzamide HDAC inhibitors ameliorates the disease phenotype of a Friedreich ataxia mouse model	Sandi, C; Pinto, RM; Al-Mahdawi, S; Ezzatizadeh, V; Barnes, G; Jones, S; Rusche, JR; Gottesfeld, JM; Pook, MA
2012	The mismatch repair system protects against intergenerational GAA repeat instability in a Friedreich ataxia mouse model	Ezzatizadeh, V; Pinto, RM; Sandi, C; Sandi, M; Al-Mahdawi, S; Te Riele, H; Pook, MA
2007	Somatic instability of the expanded GAA triplet-repeat sequence in Friedreich ataxia progresses throughout life	Pook, M A; De Biase, I; Ramussen, A; Monticelli, A; Al-Mahdawi, S; Cocozza, S; Bidichandani, S